8Discussion: According to the reports, the ""a"" determinant of
OBI patients contains
Gly145Arg/Ala/Ile/Trp/Glu (
G145R/A/I/W/E),
Leu109Arg (
L109R),
Gly119Arg (
G119R),
Pro120Thr (
P120T),
Lys122Ile (
K122I),
Thr126Asn (
T126N),
Thr127Arg (
T127R),
Gln129Asn (
Q129N),
Thr131Asn (
T131N